Monochromacy · Complete

Achromatopsia Simulated in sRGB

It is the absence of working cones altogether, so vision relies on rods, which cannot tell colors apart. It is inherited when both parents pass on the same recessive gene. It affects about 1 in 30,000 people.

Category
Monochromacy
Type
Complete
Cones
None working
Simulation
Luminance only

Live lab

Everyday interfaces with achromatopsia

Four everyday interfaces, or an image of your own, simulated as you watch. Drag the divider, change the severity, and turn on the fix to see the same interface designed so color is never the only clue.

The live lab needs JavaScript. The sections below show the same simulation, color by color.

Everyday colors

How achromatopsia changes common colors

Color disappears and only lightness is left. It usually comes with strong sensitivity to light and reduced sharpness of vision.

Each chip is the color on the left and the simulation on the right. Open one for its full page.

  • red

    #FF0000 → #7F7F7F

    ΔE2000 31.2

  • orange

    #FFA500 → #B8B8B8

    ΔE2000 28.9

  • gold

    #FFD700 → #DADADA

    ΔE2000 29.4

  • yellow

    #FFFF00 → #F7F7F7

    ΔE2000 30.5

  • lime

    #00FF00 → #DCDCDC

    ΔE2000 32.4

  • green

    #008000 → #6D6D6D

    ΔE2000 27.6

  • teal

    #008080 → #737373

    ΔE2000 21.5

  • cyan

    #00FFFF → #E5E5E5

    ΔE2000 24.9

  • blue

    #0000FF → #4C4C4C

    ΔE2000 33.4

  • navy

    #000080 → #212121

    ΔE2000 28.6

  • purple

    #800080 → #464646

    ΔE2000 27.3

  • fuchsia

    #FF00FF → #919191

    ΔE2000 32.1

  • hotpink

    #FF69B4 → #9F9F9F

    ΔE2000 26.8

  • brown

    #A52A2A → #585858

    ΔE2000 25.8

  • gray

    #808080 → #808080

    ΔE2000 0.0

Lightness

Only lightness is left

With no working cones, colors differ only in how light or dark they are. Here are the everyday colors, darkest first; those within 3 L* of each other are the same gray.

  1. Same gray

  2. Same gray

  3. Same gray

  4. Same gray

Confusions

Colors achromatopsia confuses

CSS named colors that are far apart to typical vision but nearly identical once simulated. Never tell these apart by color alone.

The cones

Rods only

Each curve is how strongly one cone pigment absorbs light across the spectrum, peaking at about 419, 531 and 558 nm. With no working cones, daylight vision falls to the rods, which cannot see color. Below the curves, the visible spectrum as typical vision and as this type see it.

400450500550600650700

Typical vision

Achromatopsia

The curves are the visual pigment template of Govardovskii et al. (2000) at the peaks Dartnall, Bowmaker and Mollon measured in human eyes. They show the pigments themselves; at the cornea the eye's lens and macular pigment shift them. Govardovskii et al. 2000 · Dartnall et al. 1983

Genes

How it is inherited

The genes behind it, where they sit, and the odds of passing it on. Pick the parents to see a Punnett square: each square is one chance in four.

Genes
CNGB3, CNGA3, GNAT2, PDE6C, PDE6H, ATF6
Where
Six genes, among them CNGB3 at 8q21.3 and CNGA3 at 2q11.2
Inheritance
Autosomal recessive
What changes
Changes in genes the cones need to turn light into a signal. CNGB3 accounts for about 60% of cases in people of European descent.

The calculator needs JavaScript.

Diagnosis

How it is tested

A screening test says that something is different; a diagnostic one says what. Only an eye care professional can diagnose a color vision deficiency. Plates on a screen, including this site's, show the idea but cannot diagnose.

TestWhat it isFor this type
Farnsworth D-15Fifteen colored caps to put in order. Almost every dichromat fails; many people with a mild anomaly pass. The pattern of errors shows the axis. Birch 2008Detects it
Nagel anomaloscopeMatch a yellow light with a mix of red and green. The reference test for red–green deficiency: it tells protan from deutan and dichromacy from anomalous trichromacy, and grades severity. Birch 2008Partly
ERG and genetic testingAn electroretinogram shows cone responses absent or much reduced, with rods near normal; a genetic test confirms the gene. Blue-cone monochromacy is told apart by its working S cones. GeneReviews: achromatopsiaDetects it

Status colors

Red, amber and green

A traffic-light status set leans entirely on hue. Give each state a word or an icon too, as WCAG 1.4.1 asks.

WCAG 1.4.1 Use of Color
  • Error
  • Warning
  • Success

Top: typical vision. Bottom: achromatopsia. The closest two status colors end up ΔE2000 10.6 apart.

Your palette

Check your colors

Paste a palette, or start from one below. The bars show the closest pair under every type; the table shows every pair under the one you pick.

The checker needs JavaScript.

Design for it

Designing so it does not matter

  1. Never let color carry meaning alone: add a label, an icon, a pattern or a position.
  2. Separate colors by lightness as well as hue, so they stay apart in every simulation.
  3. Keep text contrast at 4.5:1 or more, and 3:1 for icons and the edges of controls.
  4. Check designs with a simulator before you ship them.

Simulate a whole page in the Color Blindness Simulator, or check a pair in the Contrast Checker.

Other types

The other types